Baylor University Medical Center Proceedings April 2017 - 233


in the right bundle branch, the part of the atrioventricular
conduction system with the longest refractory period. The
distal part of the right bundle branch was depolarized late,
probably by transseptal conduction, and thus was refractory
when the next impulse arrived. Even longer runs of aberrant
ventricular conduction due to persistent functional refractoriness of the right bundle branch have been misdiagnosed as
ventricular tachycardia, an error recognized by Ashman and
his colleagues (1).
An hour after she arrived in the emergency department, the
patient spontaneously reverted to sinus rhythm. With her lying
on her left side, a soft opening snap and a low-pitched diastolic
murmur of mitral stenosis were heard, as well as a soft murmur
of mitral regurgitation. On chest radiograph, the pulmonary
arteries and the left atrial appendage were large and produced
a straight left heart border.
A transthoracic echo-Doppler study demonstrated a dilated
left atrium with an anteroposterior diameter of 5.6 cm (reference,

April 2017

1.9-4.0). The other chamber sizes were normal. The thicknesses
of the ventricular septum and left ventricular posterior wall
(1.2 cm) were just above the upper limit of normal. The mitral valvular leaflets were thick, calcified, and noncompliant.
The peak diastolic pressure gradient across the mitral valve was
20 mm Hg with a mean gradient of 9 mm Hg. The mitral
valvular orifice area was 0.8 cm2 both by measurement of the
two-dimensional image and by the pressure halftime. Left and
right ventricular systolic function were normal. Mild mitral
and tricuspid regurgitation were noted, and pulmonary arterial
systolic pressure was 60 mm Hg (reference, 15-30). Cardiac
catheterization confirmed the echocardiographic findings,
and coronary arteriography was normal. Mitral valve replacement with a 33 mm St. Jude mechanical prosthesis and the
postoperative course were uneventful.
1.

Gouaux JL, Ashman R. Auricular fibrillation with aberration simulating
ventricular paroxysmal tachycardia. Am Heart J 1947;34(3):366-373.

Atrial fibrillation 50 years after acute rheumatic fever as the first manifestation of rheumatic mitral stenosis

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